Infant-onset degos disease with nervous system involvement and a literature review (May 2024) DOI: 10.3389/fped.2024.1374150

Critical Management Of A Patient With Degos Disease Involving Small Bowel And Stomach Perforations (January 2024) DOI: 10.1097/01.ccm.0001003896.79101.d5

Increased type I interferon expression from T cells in lesional skin of Degos disease (May 2023) DOI: 10.1111/1346-8138.16727

Atrophic papulosis (Köhlmeier-Degos disease) in children and adolescents-A cross-sectional study and literature review (January 2023) DOI: 10.1111/jdv.18844

Laparoscopic detection of malignant atrophic papulosis (MAP) in a Paediatric patient(December 2022) DOI: 10.1111/jdv.18446

Inflammation and thrombo-occlusive vessel signalling in benign atrophic papulosis (Köhlmeier-Degos disease) (Nov 2022)DOI: 10.1111/jdv.18362

Interferon receptor dysfunction in a child with malignant atrophic papulosis and CNS involvement (August 2022)DOI: 10.1016/S1474-4422(22)00167-3

A Particular Bicentric Structure in Dermoscopic Demonstration of Degos Disease (July 2022) DOI: 10.5826/dpc.1203a96

Atrophic papulosis (Köhlmeier-Degos disease) revisited: a cross-sectional study on 105 patients (June 2022)DOI: 10.1111/jdv.18260

Gastrointestinal Kohlmeier–Degos disease: a narrative review (April 2022) DOI: 10.1186/s13023-022-02322-9

Exploring the pathophysiologic basis of constrictive pericarditis of Kohlmeier Degos disease: A case series and review of the literature (March 2022) DOI: 10.1016/j.anndiagpath.2022.151943

Neurological Involvement in Malignant Atrophic Papulosis: A Comprehensive Review of Literature (February 2022) DOI: 10.4103/0028-3886.338719

Clinical manifestations and treatment outcomes in degos disease: a systematic review (May 2021) DOI: 10.1111/jdv.17311

Clinico-Pathological Features in Köhlmeier-Degos Disease with Cutaneous and Neurological Involvement (March 2021) DOI: 10.4103/aian.aian_1004_20

Degos-like lesions as a cutaneous manifestation of cytomegalovirus infection: A rare and serious complication in a patient with drug-induced hypersensitivity syndrome (December 2020) DOI: 10.1111/1346-8138.15717

Degos disease: a case report and review of the literature (October 2020) DOI: 10.1186/s13256-020-02514-6

Malignant Atrophic Papulosis (August 2020) Bookshelf ID: NBK544329

Degos disease: A radiological-pathological correlation of the neuroradiological aspects of the disease (May 2020) DOI: 10.1016/j.anndiagpath.2020.151545

Degos-Like Cutaneous Findings in an Adult Woman With NXP-2-Associated Dermatomyositis (February 2020) DOI: 10.1001/jamadermatol.2019.3940

Chronic pleuritis leading to severe pulmonary restriction: a rare complication of Degos disease (December 2019) DOI: 10.1136/bcr-2019-232759

Degos Disease: an update (December 2019) DOI: https://emedicine.medscape.com/article/1087180-overview?form=fpf

Enhanced cutaneous Rock2 expression as a marker of Rho Kinase pathway activation in autoimmune disease and Kohlemeier-Degos disease (October 2019) DOI: 10.1016/j.anndiagpath.2019.151414

Disseminated discoid lupus erythematosus mimicking Degos disease (August 2019) DOI: 10.1111/ajd.13139

The color of skin: white diseases of the skin, nails, and mucosa (July 2019) DOI: 10.1016/j.clindermatol.2019.07.018

Dramatic neurological debut in a case of Köhlmeier-Degos disease (June 2019) DOI: 10.1007/s10072-019-03952-x

Kohlmeier-Degos disease with constrictive pericarditis and atrial fibrillation (July 2018) DOI: 10.1007/s12574-018-0386-4

Pediatric Malignant Atrophic Papulosis (April 2018) DOI: 10.1542/peds.2016-4206

Malignant atrophic papulosis with motor aphasia and intestinal perforation: A case report and review of published works (March 2018) DOI: 10.1111/1346-8138.14280

The evolution of cerebrovascular changes in Köhlmeier-Degos disease: An 11-year follow-up case report (November 2017) DOI: 10.1016/j.jocn.2017.11.006

Benign atrophic papulosis (Kohlmeier–Degos disease): the wedge-shaped dermal necrosis can resolve with time (June 2017) DOI: 10.1111/jdv.14355

Diffuse atrophic papules and plaques, intermittent abdominal pain, paresthesias, and cardiac abnormalities in a 55-year-old woman (December 2016) DOI: 10.1016/j.jaad.2016.09.015

Degos disease mimicking primary vasculitis of the CNS (April 2016) DOI: 10.1212/NXI.0000000000000206

Bowel perforation in Dego’s disease: a lethal surgical scenario (January 2016) DOI: 10.18203/2349-2902.isj20151489

Laparoscopy shows superiority over endoscopy for early detection of malignant atrophic papulosis gastrointestinal complications: a case report and review of literature (November 2015) DOI: 10.1186/s12876-015-0387-y

Aspirin in dermatology: Revisited (November 2015) DOI: 10.4103/2229-5178.169731

Acquired neurocutaneous disorders (November 2015) DOI: 10.1016/B978-0-444-62702-5.00003-2

Degos disease – malignant atrophic papulosis or cutaneointestinal lethal syndrome: rarity of the disease (April 2015) DOI: 10.2147/CEG.S59794

Renal involvement in Malignant Atrophic Papulosis (Degos Disease) (March - April 2015) DOI: 10.1590/abd1806-4841.20153839

Degos Disease Associated with Behçet’s Disease (March 2015) DOI: 10.5021/ad.2015.27.2.235

Degos disease: report of a case and review of the literature (February 2015) PMID: 25686287

Challenging mimickers of primary systemic vasculitis (December 2014) DOI: 10.1016/j.rdc.2014.09.011

Non-atherosclerotic Causes of Mesenteric Arterial Disease (October 2014) DOI: 10.1007/978-1-4939-1847-8_10

Malignant Atrophic Papulosis Is Challenging to Diagnose, Treat (July 2014) ID: https://www.the-rheumatologist.org/article/malignant-atrophic-papulosis-is-challenging-to-diagnose-treat/?singlepage=1

Case 18-2014 — A 32-Year-Old Man with a Rash, Myalgia, and Weakness (June 2014) DOI: 10.1056/NEJMcpc1304161

Severe Neurologic Involvement of Degos Disease in a Pediatric Patient (April 2014) DOI: 10.1177/0883073812474692

Malignant and benign forms of atrophic papulosis (Köhlmeier-Degos disease): systemic involvement determines the prognosis (January 2014) DOI: 10.1111/bjd.12642

The effects of Eculizumab on the pathology of malignant atrophic papulosis (November 2013) DOI: 10.1186/1750-1172-8-185

A case of Degos disease: demonstration of C5b-9-mediated vascular injury (April 2013) DOI: 10.3109/14397595.2013.874761

Effective treatment of malignant atrophic papulosis (Köhlmeier-Degos disease) with treprostinil--early experience (April 2013) DOI: 10.1186/1750-1172-8-52

Malignant atrophic papulosis (Köhlmeier-Degos disease) – A review (January 2013) DOI: 10.1186/1750-1172-8-10

A case of Degos disease successfully treated with corticosteroid combined with cyclophosphamide (July 2012) DOI: 10.1007/s00296-010-1436-z

A fatal case of Degos’ disease which presented with recurrent intestinal perforation (October 2011) DOI: 10.4240/wjgs.v3.i10.156

LETHAL SYSTEMIC DEGOS DISEASE WITH PROMINENT CARDIO-PULMONARY INVOLVEMENT (September - October 2011) DOI: 10.4103/0019-5154.87157

Commentary on ‘Degos disease: a C5b-9/interferon-α-mediated endotheliopathy syndrome’ by Magro et al: a reconsideration of Degos disease as hematologic or endothelial genetic disease (August 2011) DOI: 10.5070/D309r396d1

Lack of recurrence of malignant atrophic papulosis of Degos in multivisceral transplant: insights into possible pathogenesis? (August 2011) DOI: 10.1016/j.jaad.2010.12.021

Malignant atrophic papulosis as an incidental finding on laparoscopy–case report (August 2011) DOI: 10.1055/s-0030-1262679

Degos Disease with Dermatomyositis-like Phenomenon: A Diagnostic Dilemma and a Therapeutic Challenge (May - June 2011) DOI: 10.2310/7750.2011.10035

A man with generalized small white skin lesions and abdominal pain (May 2011) DOI: 10.1111/j.1365-4632.2010.04603.x

Degos Disease A C5b-9/Interferon-α–Mediated Endotheliopathy Syndrome (April 2011) DOI: 10.1309/AJCP66QIMFARLZKI

Degos-Like Lesions Associated with Systemic Lupus Erythematosus (April 2011) DOI: 10.5021/ad.2017.29.2.215

Infantile neurological Degos disease (March 2011) DOI: 10.1016/j.ejpn.2010.06.003

Case report Cutaneous-limited Degos disease – benign variant or distinctive clinical entity? (January 2011) ID: http://www.termedia.pl/Case-report-Cutaneous-limited-Degos-disease-benign-variant-or-distinctive-clinical-entity-,7,16317,0,0.html

Post-streptococcal vasculopathy with evolution to Degosâ€™ disease (January 2011) DOI: 10.1016/j.jns.2010.10.007

Malignant Atrophic Papulosis: A Case Report with Severe Visual and Neurological Impairment (December 2010) DOI: 10.1111/j.1525-1470.2010.01287.x

Malignant Atrophic Papulosis with Severe Gastrointestinal Perforation and Omental Necrosis: a Case Report (May - June 2010) DOI: 10.1177/147323001003800346

Degos cutaneous disease with features of connective tissue disease (April 2010) DOI: 10.1097/RHU.0b013e3181d5362e

[Case of disseminated intestinal and cutaneous thromboangiitis (Kohlmeier-Degosâ€™ syndrome)] (January 2010) PMID: 20387678

Degos disease: considerations for reclassification (September 2009) DOI: 10.1016/j.jaad.2009.03.028

Köhlmeier-Degos Disease (malignant atrophic papulosis) and Neurologic Involvement. Doença de Köhlmeier-Degos (papulose atrófica maligna) e envolvimento neurológico (September 2009) DOI: 10.1590/S0004-282X2009000400022

Degos’ disease: a rare condition simulating rheumatic diseases (July 2009) DOI: 10.1007/s10067-009-1164-5

Wegener’s granulomatosis: a new entity in the growing differential diagnosis of Degos disease (July 2009) DOI: 10.1111/j.1365-2230.2008.02953.x

Atrophic scars in a 54-year-old woman (March 2009) DOI: 10.1001/archdermatol.2008.627-a

Malignant Atrophic Papulosis (MAP, Degos’ disease) (March 2009) PMID: 19249895

Pairing and comparing nine diseases with Degos Disease (Malignant Atrophic Papulosis): An attempt to illustrate our understanding and direct future inquiry (2009) DOI: 10.5070/D381n2q8zd

Painless pink papules with central porcelain-white scars (November 2008) DOI: 10.1503/cmaj.080373

Clinical challenges and images in GI. Image 2: Malignant atrophic papulosis (Degos’ disease) with systemic manifestations (October 2008) DOI: 10.1053/j.gastro.2008.10.009

Parvovirus B19-associated catastrophic endothelialitis with a Degos-like presentation (October 2008) DOI: 10.1111/j.1600-0560.2007.00974.x

Degos’ disease (malignant atrophic papulosis) as a fatal cause of acute abdomen: report of a case (August 2008) DOI: 10.1007/s00595-007-3728-9

Inefficacy of intravenous immunoglobulins and infliximab in Degos’ disease (March - April 2008) DOI: 10.1179/acb.2008.63.2.007

A Case of Systemic Lupus Erythematosus with Degos’ Disease (September 2007) ID: https://www.jrd.or.kr/journal/view.html?volume=14&number=3&spage=256

Generalized red papules with gastrointestinal complications. Diagnosis: malignant atrophic papulosis (Degos’ disease) (September 2007) DOI: 10.1111/j.1365-2230.2007.02403.x

The use of intravenous immunoglobulin in cutaneous and recurrent perforating intestinal Degos disease (malignant atrophic papulosis) (June 2007) DOI: 10.1111/j.1365-2133.2007.07951.x

Benign cutaneous Degos disease in a 16-year-old girl (January - February 2007) DOI: 10.1111/j.1525-1470.2007.00326.x

Degos’ disease and abnormal MRI (December 2006) ID: https://strokenotes.blogspot.com/2007/01/degos-disease-and-abnormal-mri.html

Degos’ disease: Acute abdomen with skin rash (July - August 2006) PMID: 16974032

Malignant atrophic papulosis: endocardial involvement and positive anticardiolipin antibodies (May 2006) DOI: 10.1111/j.1468-3083.2006.01339.x

A fatal case of malignant atrophic papulosis (Degos' disease) in a man with factor V Leinden mutation and lupus anticoagulant (May 2006) DOI: 10.2340/00015555-0068

Optic nerve and spinal cord manifestations of malignant atrophic papulosis (Degos disease) (February 2006) DOI: 10.1136/jnnp.2005.066134

Degos disease associated with protein S deficiency (September 2005) DOI: 10.1111/j.1365-2133.2005.06764.x

Painful penile ulceration in a patient with malignant atrophic papulosis (September 2005) DOI: 10.1111/j.1468-3083.2005.01227.x

Benign cutaneous Degos disease (July 2005) DOI: 10.1111/j.1365-463.2004.02080.x

Degos disease with an inconspicuous clinical course (July 2005) DOI: 10.1111/j.1468-3083.2004.01181.x

Nervous System Involvement in Degos’ Disease (March 2005) PMID: 15760880

A case of Systemic Malignant Atrophic Papulosis (Köhlmeier-Degos’ Disease) (March 2005) PMID: 15779511

Lesions resembling malignant atrophic papulosis in a patient with progressive systemic sclerosis (February 2005) PMID: 15773530

Degos’ disease is probably a distinct entity: A review of clinical and laboratory evidence (February 2005) DOI: 10.1016/j.jaad.2004.06.049

Is Degos’ Disease a clinical and histological end point rather than a specific disease? (June 2004) DOI: 10.1016/j.jaad.2003.11.063

Inflammatory linear vasculopathy mimicking Degos’ disease (June 2004) DOI: 10.1111/j.1365-2133.2004.06020.x

A case of malignant atrophic papulosis successfully treated with nicotine patches (September 2003) DOI: 10.1046/j.1365-2133.2003.05508.x

Malignant atrophic papulosis. Report of a case with multiple ophthalmic findings (September 2003) PMID: 14601855

Degos’ Disease: a distinctive pattern of disease, chiefly of lupus erythematosus, and not a specific disease per se (August 2003) DOI: 10.1097/00000372-200308000-00005

Benign course of malignant atrophic papulosis (Kohlmeier-Degos disease): lack of vessel occlusion as good prognostic sign? (May 2003) DOI: 10.1046/j.1610-0387.2003.02015.x

Presentation of Degos Syndrome as Acute Small-Bowel Perforation (January 2003) DOI: 10.1001/archsurg.138.1.57

Benign Degos’ disease developing during pregnancy and followed for 10 years (October 2022) DOI: 10.1080/000155502320323261

Malignant atrophic papulosis in an infant (May 2002) DOI: 10.1046/j.1365-2133.2002.04677.x

Papulosis maligna atrophicans Degos Nicht immer maligne! (January 2002) DOI: 10.1007/s105-002-8047-8

Degos’ disease (December 2001) DOI: 10.1046/j.1365-4362.2000.00828.x

Papulosis maligna atrophicans (Köhlmeier-Degos) Diagnose, Therapie, Verlauf (August 2001) DOI: 10.1007/s001050170092

Benign Cutaneous Degos Disease: a case report with emphasis on histopathology as papules chronologically evolve (April 2001) DOI: 10.1097/00000372-200104000-00006

Malignant atrophic papulosis (Degos’ disease): clinicopathological correlations (January 2001) DOI: 10.1046/j.1468-3083.2001.00216.x

Posterior subcapsular cataract in Degos disease (June 2000) DOI: 10.1016/s0002-9394(00)00460-8

Degos’ disease with constrictive pericarditis: a case report (June 2000) DOI: 10.1253/jcj.64.464

Malignant Atrophic Papulosis (1998) PMID: 20921728

Köhlmeier-Degos’s disease with primary intestinal manifestation (October 1997) DOI: 10.3109/00365529709011226

CENTER SECTION OF THE SPANISH ACADEMY OF DERMATOLOGY AND VENEREOLOGY (January 1997) PMID: 13003422

Small bowel fistulae in Degos’ disease: a case report and literature review (October 1996) PMID: 8855750

Skin lesion with a fatal neurologic outcome (Degos’ disease) (March 1996) DOI: 10.1212/wnl.46.3.636

Absence of antiphospholipid and anti-endothelial cell antibodies in malignant atrophic papulosis: a study of 15 cases (November 1995) DOI: 10.1016/0190-9622(95)91843-4

Report of a case of malignant atrophic papulosis or Degos disease (March 1994) PMID: 8060787

Malignant atrophic papulosis. A report of two cases with altered fibrinolysis and platelet function (September 1993) DOI: 10.1111/j.1365-2230.1993.tb02246.x

Degos disease: a new simulator of non-accidental injury (August 1991) DOI: 10.1289/ehp.94-1567959

An atypical paediatric case of malignant atrophic papulosis (Köhlmeier-Degos disease) (April 1990) DOI: 10.1007/BF01959394

The pathology and pathogenesis of malignant atrophic papulosis (Degos’ disease). A case study with reference to other vascular disorders (February 1987) DOI: 10.1016/S0344-0338(87)80148-6

Familial malignant atrophic papulosis (Degos’ disease)–additional evidence for heredity and a benign course (January 1986) DOI: 10.1111/j.1365-2133.1986.tb02789.x

Six cases of malignant atrophic papulosis (Degos’ disease) occurring in one family (October 1984) DOI: 10.1111/j.1365-2133.1984.tb06611.x

[Familial Degos' atrophic papulosis (mother-daughter)] (1984) PMID: 6721361

Childhood Kohlmeier-Degos disease with atypical skin lesions (September 1983) DOI: 10.1212/wnl.33.9.1146

Malignant atrophic papulosis (January 1979) DOI: 10.1111/j.1365-2133.1979.tb03566.x

Malignant atrophying papulosis (Degos’ disease) (author’s translation) (August - September 1978) PMID: 153724

Unconventional Viruses and the Origin and Disappearance of Kuru (September 1977) DOI: 10.1126/science.142303

Degos’ Disease (Papulosis Atrophicans Maligna): Report of a Case with Degenerative Disease of the Central Nervous System (January 1962) DOI: 10.1097/00007611-196201000-00014

Research Articles